Detection of Organic Acidemias in Brazil

Moaçir Wajner , Kimiyo Raymond , Alethéa Barschak , Ana Paula Luft
Archives of Medical Research 33 ( 6) 581 -585

12
2002
Inhibition of citrate oxidation in vitro by 2-hydroxybutyrate and 4-hydroxybutyrate in cerebral cortex of young rats

CARLOS S. DUTRA-FILHO , MOACIR WAJNER , CLÓVIS M. D. WANNMACHER , EDSON GASSEN
Biochemical Society Transactions 23 ( 2)

3
1995
2-Hydroxybutyrate and 4-hydroxybutyrate inhibit CO2 formation from labeled substrates by rat cerebral cortex.

CARLOS S. DUTRA-FILHO , MOACIR WAJNER , CLóVIS M. D. WANNMACHER , EDSON GASSEN
Biochemical Society Transactions 23 ( 2)

13
1995
Immunomodulatory action of amino acids on lymphocyte blastogenesis.

MÁRCIA H. SOMMER , MÁRCIA H. XAVIER , MARCELO B. FIALHO , CLÓVIS M. D. WANNMACHER
Biochemical Society Transactions 20 ( 2)

1
1992
Intrastriatal administration of 3-hydroxyglutaric acid induces convulsions and striatal lesions in rats.

Carlos F de Mello , Stefan Kölker , Barbara Ahlemeyer , Fabiane R de Souza
Brain Research 916 ( 1) 70 -75

43
2001
Alterations in lipid profile and enzymes paraoxonase and butyrylcholinesterase in CBS-deficient patients

Camila Vanzin , Carmen Vargas , Célia Nogueira , Laura Vilarinho
10th International Symposium SPDM, 20-21Março 2014

2014
Evidência de que os ácidos β-hidroxibutirato e acetoacetato não causam estresse oxidativo em córtex cerebral de ratos jovens in vitro

Carolina Gonçalves Fernandes , Luciana De Bortoli da Silva , ALlana Pimentel Moura , Ana Paula BESKOw
Revista de Iniciação Científica da ULBRA 7 ( 7)

2008
Inibição da atividade da Na+, K+-ATPase pelo ácido fitânico em cerebelo de ratos é provavelmente causada pela alteração da fluidez da membrana sináptica

Carolina Viegas , Anelise Tonin , Cezar Ribeiro , Vannessa Gonçalves Araujo Lobato
XVIII SALÃO DE INICIAÇÃO CIENTÍFICA E TECNOLÓGICA

2012
Experimental evidence that lipid and protein oxidative damage are induced in blood of MCAD deficient patients

Caroline P. Mescka , Giovana B. Biancini , Giovanna Negretto , Moacir Wajner
Molecular Genetics and Metabolism 105 ( 3) 313 -313

2012
Ethylmalonic acid impairs bioenergetics by disturbing succinate and glutamate oxidation and induces mitochondrial permeability transition pore opening in rat cerebellum

Leonardo de Moura Alvorcem , Bianca Seminotti , Fabrício Figueiró , Geancarlo Zanatta
Journal of Neurochemistry

2021
Evidence that the inhibitory effects of guanidinoacetate on the activities of the respiratory chain, Na+,K+-ATPase and creatine kinase can be differentially prevented by taurine and vitamins E and C administration in rat striatum in vivo

Alexandra I. Zugno , Emilene B.S. Scherer , Cristiane Mattos , César A.J. Ribeiro
Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease 1772 ( 5) 563 -569

18
2007
l-Carnitine prevents oxidative stress in striatum of glutaryl-CoA dehydrogenase deficient mice submitted to lysine overload.

Gilian Guerreiro , Alexandre U. Amaral , Rafael Teixeira Ribeiro , Jéssica Faverzani
Biochimica et Biophysica Acta 1865 ( 9) 2420 -2427

2
2019
Disturbance of bioenergetics and calcium homeostasis provoked by metabolites accumulating in propionic acidemia in heart mitochondria of developing rats.

Ana Cristina Roginski , Alessandro Wajner , Cristiane Cecatto , Simone Magagnin Wajner
Biochimica et Biophysica Acta 1866 ( 5) 165682

1
2020
Sulfite disrupts brain mitochondrial energy homeostasis and induces mitochondrial permeability transition pore opening via thiol group modification

Mateus Grings , Alana P Moura , Alexandre U Amaral , Belisa Parmeggiani
Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease 1842 ( 9) 1413 -1422

28
2014
Mitochondrial bioenergetics deregulation caused by long-chain 3-hydroxy fatty acids accumulating in LCHAD and MTP deficiencies in rat brain: a possible role of mPTP opening as a pathomechanism in these disorders?

Anelise Miotti Tonin , Alexandre Umpierrez Amaral , Estela Natacha Busanello , Juciano Gasparotto
Biochimica et Biophysica Acta 1842 ( 9) 1658 -1667

16
2014
Disturbance of energy and redox homeostasis and reduction of Na+,K+-ATPase activity provoked by in vivo intracerebral administration of ethylmalonic acid to young rats.

Luciana Ritter , Daniele Kleemann , Fernanda Hermes Hickmann , Alexandre Umpierrez Amaral
Biochimica et Biophysica Acta 1852 ( 5) 759 -767

13
2015
Signaling mechanisms underlying the glioprotective effects of resveratrol against mitochondrial dysfunction.

Bruna Bellaver , Larissa Daniele Bobermin , Débora Guerini Souza , Marília Danielly Nunes Rodrigues
Biochimica et Biophysica Acta 1862 ( 9) 1827 -1838

23
2016