Pallidal deep brain stimulation for the treatment of DYT6 dystonia: a case report and review of literature.
作者： Gholam Ali Shahidi , Mohammad Rohani , Shahnaz Miri , Mansour Parvaresh
DOI:
关键词: One year follow up 、 Pathology 、 Treatment outcome 、 Male patient 、 Medicine 、 Globus pallidus internus 、 Dystonia 、 Anesthesia 、 Effective treatment 、 Swallowing 、 Deep brain stimulation
摘要: Little is known about the results of pallidal deep brain stimulation (DBS) in DYT6 dystonia. This will be first report dystonia treated with DBS from Iran. A 21 years old male patient underwent bilateral stimulation. The target was sensorimotor region posteroventral globus pallidus internus (GPi). parameters included an amplitude 2.7 V, frequency 160 Hz, and pulse width 90 μs which were adjusted according to patient's response 12 months after surgery. Treatment outcome measured by patient’s Burke-Fahn-Marsden Dystonia Rating Scale (BFMDRS) score. Before surgery, BFMDRS score 32. However, reduced 7 at one year follow up surgery (78% improvement total score). Dystonic symptoms extremities mouth completely resolved. Also speech swallowing function significantly improved. Although previous observations reported a poor moderate speech, we found as effective treatment not only for dystonic features, but also
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