Right Ventricular Cardiomyopathy and Sudden Death in Young People

摘要: Abstract From 1979 to 1986, we conducted postmortem studies of 60 persons under 35 years age who had died suddenly in the Veneto Region northeastern Italy. Unexpectedly, found that 12 subjects — 7 males and 5 females ranging from 13 30 morphologic features right ventricular cardiomyopathy. This disorder not been diagnosed or suspected before died. In five cases, sudden death was first sign disease; remaining seven a history palpitations, syncopal episodes, both, those seven, arrhythmias previously recorded on electrocardiographic examination. Ten during exertion. At autopsy, subjects' heart weights were normal moderately increased. Two main histologic patterns identified lipomatous transformation fibrolipomatous free wall (6 cases each); all left ventricle substantially spared. Signs m...