Bilateral Striatal Necrosis after Sydenham's Chorea in a 7-Year-Old Boy: A 2-Year Follow-Up

摘要: Child bilateral striatal necrosis (BSN) is a rare and etiologically heterogeneous condition. An association with group A streptococcus (GAS) infection was previously reported in two cases of BSN infancy early childhood. We here report on 7-year-old boy who developed chorea dystonia 20 days after symptomatic recovery from Sydenham's chorea. Repeated brain magnetic resonance imaging scans, obtained before, soon the onset post-Sydenham symptoms, 1 year later were consistent an evolution microbleeding to necrosis, consequently reduced basal ganglia volume enlargement frontal horns. No support found for other possible autoimmune, infectious, metabolic, toxic or genetic etiologies BSN. Prednisone treatment instituted continued 1 year. Two years child, although much improved, still has generalized dystonic–choreic movements. This case confirms extends into school age, link between GAS