The etiology, clinical presentation, and management of pseudomyxoma peritonei.

摘要: PMP is a rare condition, which, although of "borderline malignancy," invariably fatal. Difficulties exist with the definition PMP. It has been broadly applied to include heterogenous group pathologic lesions that present clinically "jelly belly" due mucinous ascites. The relatively few reports in literature commonly use different definitions, and there no consensus on point separation between carcinomatosis secondary adenocarcinoma. Sugarbaker suggested "the term pseudomyxoma peritonei syndrome be strictly pathologically prognostically homogenous cases characterized by histologically benign peritoneal tumors are frequently associated an appendiceal adenoma." This excludes all optimal treatment undoubtedly complete tumor excision, complex surgical peritonectomy procedures, taking average 10 hours. Surgery usually combined intraperitoneal, now intraoperative heated chemotherapy. These techniques have high morbidity mortality. rarity together risks definitive treatment, suggests such ought centralized centers, covering large population. search continues for safer, less aggressive treatments, but hampered lack hard evidence absence experimental animal or human models evaluate emerging strategies.