Insights into the molecular basis of polyglutamine neurodegeneration from studies of a spinocerebellar ataxia type 7 mouse model.
作者： S.K. Grote , A.R. La Spada
DOI: 10.1159/000072851
关键词: Spinocerebellar ataxia 、 Biology 、 Neurodegeneration 、 Genetics
摘要: Spinocerebellar ataxia type 7 (SCA7) is one member of a growing list neurodegenerative disorders that are all caused by CAG repeat expansions produce disease encoding elongated polyglutamin
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