Pseudo Prune Belly syndrome: a case report with unilateral abdominal defect.
作者： Giuseppe De Bernardo , Maurizio Giordano , Daniele De Brasi , Francesco Esposito , Rita De Santis
DOI: 10.1016/J.RADCR.2019.05.019
关键词: Prune belly syndrome 、 Abdominal Hernia 、 Anatomy 、 Urinary system 、 Diastasis recti 、 Rib cage 、 Abdominal wall 、 Magnetic resonance imaging 、 Diastasis 、 Medicine
摘要: Prune Belly syndrome occurs in 1/40,000 live births and predominantly males. It is characterized by triad: cryptorchidism, abdominal wall, urinary tract abnormalities. Patients with partial or unilateral wall deficiency, undescended testis, female neonates laxity are classified as Pseudo syndrome. In the 3%-5% of patients affected syndrome, indeed case reports available very few. We described a male patient born large hernia. Thoracoabdominal X-ray confirmed hernia revealed malformation rib cage curved ribs. Magnetic resonance imaging showed thinning ultrasonography detected rectus oblique muscles hypoplastic diastasis stretching Hunter's line. Cryptorchidism abnormalities were not detected. The first surgical operation was performed at 2 years life when general conditions stable.
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