Pulmonary alveolar proteinosis in association with Fanconi's anemia and psoriasis. A possible common pathogenetic mechanism.
作者： Rodney D. Steens , Quentin A. Summers , Richard A. Tarala
关键词: Etiology 、 Lung Disorder 、 Respiratory disease 、 Psoriasis 、 Pulmonary alveolar proteinosis 、 Fanconi anemia 、 Pathology 、 Lung 、 Anemia 、 Medicine 、 Immunology
摘要: We report a case of PAP which proved to be fatal despite whole lung lavage. The need for early BAL and transbronchial biopsies in diffuse infiltrative disorders unknown etiology is highlighted. occurrence association with Fanconi's anemia psoriasis raises the possibility common pathogenetic defect may related abnormal cytokine metabolism. Investigation metabolism warranted.
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