Elongation of very long-chain fatty acids is enhanced in X-linked adrenoleukodystrophy
作者： Stephan Kemp , Fredoen Valianpour , Simone Denis , Rob Ofman , Robert-Jan Sanders
DOI: 10.1016/J.YMGME.2004.09.015
关键词: Elongation 、 X-linked adrenoleukodystrophy 、 Adrenoleukodystrophy 、 Very long chain 、 Progressive neurodegenerative disorder 、 Lorenzo's oil 、 Peroxisome 、 Biosynthesis 、 Biochemistry 、 Chemistry
摘要: … from increased elongation of long-chain and very long-chain fatty acids to fatty acid species … provide more substrate for the microsomal fatty acid elongation machinery. In the second …
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