Sphincterplasty for Velopharyngeal Insufficiency in the Child Without a Cleft-Palate: Etiologies and Speech Outcomes.

作者: Michael S. Golinko , Kazlin Mason , Katie Nett , John E. Riski , Joseph K. Williams

DOI: 10.1097/SCS.0000000000001967

关键词: Velopharyngeal SphincterTrisomyVelopharyngeal insufficiencyPharynxNasalanceEtiologyAbnormalityMedicineSurgeryIntelligibility (communication)

摘要: The aim of this study is to report on speech outcomes following surgery for velopharyngeal insufficiency (VPI) a broad spectrum patients without cleft palate. Inclusion criteria included palate operated by single surgeon (JKW) over 10-year period and postoperative evaluation within 1 year. All underwent sphincter pharyngoplasty. main outcome measures were perceptual assessment using 6-point scale (1 = none or normal, 6 severe); function (VPF) adequate, 2 marginal, 3 =  dequate); quantitative nasalance score. Forty children (mean age 7.5 y) included. Eight unique conditions identified; the most common was 22q deletion syndromes (27.5%). had deep nasopharynx, mean nasopharyngeal depth >0.67. Two novel cases are presented in each child with mosaic Trisomy 14 ring chromosome 18 abnormality. Of all patients, 87.5% improved their hypernasality Preoperatively, either marginal inadequate VPF (2 3). Postoperatively, 90% (n 36) achieved adequate velar function, remainder did not improve at first evaluation. Intelligibility audible nasal emissions between 57% 65% patients. Articulation proficiency only rating initially, but then so recent This demonstrates successful diverse group It also increases awareness noncleft VPI amenable surgical correction.

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