von Willebrand's disease and hemorrhagic telangiectasia
作者： David J. Ahr , Frederick R. Rickles , Leon W. Hoyer , Dennis S. O'Leary , Marcel E. Conrad
DOI: 10.1016/0002-9343(77)90846-4
关键词: Medicine 、 Internal medicine 、 Factor VIII Activity 、 Disease 、 Gastroenterology 、 Gastrointestinal bleeding 、 Telangiectasia 、 Factor VIII antigen 、 Von Willebrand factor 、 Hemostasis 、 Pathology 、 Von willebrand 、 General Medicine
摘要: Abstract The clinical and laboratory findings in a patient with uncontrolled gastrointestinal bleeding secondary to combined hemostatic defects (von Willebrand's disease hemorrhaglc telanglectasia) are described. Evidence for von was found five family members, but no other affected relative have telangiectasla. Complete assessment of the her included determination factor VIII activity, antigen Willebrand levels. described also evaluated response transfusion utilizing these same measurements. Previous reports coexistence hereditary hemorrhagic telangiectasia reviewed. importance complete evaluation patients mucocutaneous is stressed light current knowledge diagnostic specificity available tests.
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