Cherubism and its charlatans

作者: Declan A. Lannon , Michael J. Earley

DOI: 10.1054/BJPS.2001.3701

关键词: Central giant-cell granulomaCherubismGiant cellInvolution (medicine)MedicinePathologySH3BP2Diagnostico diferencialMaxillaVariable Expression

摘要: Cherubism is a rare hereditary condition characterised by progressive cystic proliferation of the mandible and maxilla in childhood, followed post-pubertal involution process jaw remodelling adulthood. Its name derived from cherubic appearance that results hypertrophy. Here, we present case young boy with cherubism, context his pedigree, to illustrate clinical characteristics their variable expression. We also seek distinguish cherubism central giant cell granuloma tumour jaws, which it holds false synonymity.

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