Multiple cutaneous and uterine leiomyomatosis syndrome: a review.
作者： Daniele Torchia , Paolo Romanelli , Sonal Choudhary , Michael McLeod
DOI:
关键词: Leiomyomatosis 、 Biopsy 、 Hereditary leiomyomatosis and renal cell carcinoma 、 Autosomal dominant trait 、 Pathology 、 Medicine 、 Renal cell carcinoma 、 Tumor size 、 Uterus 、 Uterine fibroids
摘要: Multiple cutaneous and uterine leiomyomatosis is an autosomal dominant disease characterized by leiomyomas of the skin uterus. A small proportion patients affected multiple will develop renal cell carcinoma this condition known as hereditary carcinoma. Diagnosis usually occurs during histological analysis a biopsy. Management should involve multidisciplinary team along with periodical radiological studies to closely monitor tumor size in uterus kidneys. Gonadotropin-releasing hormone analogues are helpful reducing fibroids.
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