Anomalies of intestinal rotation and fixation: consequences of late diagnosis beyond two years of age.

摘要: The malrotation and no well fixation anomalies of the digestive tract is also frequent in older child, young adult, with characteristic specific clinical presentation. Actually, diagnostic treatment seem to be late, after suffering prolonged symptoms and/or emergency. We present nine cases embryonic development which were diagnosed treated infants or young, all above 2 years old. Eight more less complete intestinal malrotation; one them was a an intrinsic duodenal stenosis associated (no bands Ladd) another right paramesocolic hernia, always accompanied by malrotation. association other extra-digestive anomalies, especially urological, 70%. predominant symptom intermittent abdominal pain (IAP)—80%—sometimes vomiting (35%) episodes diarrhoea (25%). In cases, while background early, diagnosis late. Indeed, 60% made intra-operatively emergency surgical interventions. imaging procedures employed scanning Doppler ultrasound, CT scan, contrast gastrointestinal series (GIS). Up 30% errors interpretation occurred, although they eventually corrected tests. most reliable GIS scan contrast, partial occurred latter procedure. Surgery essential 80% pre-operative two it required as preventative measure. Post-operatively, there notable persistence SBS necrosis, lesser rest. conclude that: malrotations malfixations are still being very serious systemic consequences such obstructions necroses, suffering. This could avoided if attention paid IAP, subocclusion phenomena (distension,...), together with, case doubt about findings previous procedures, opportune tests (e.g., barium GIS). Unlike authors, we consider that morbidity/mortality late these high, calls for earlier treatment.