Constrictive pericarditis as an emerging manifestation of hyper-IgG4 disease.

摘要: A 68-year-old Japanese man was admitted for evaluation of right pleural effusion and bilateral leg edema that had progressively worsened over 6 months. As chest computed tomography revealed marked pericardial thickening, we performed a pericardiectomy, resulting in the remarkable improvement his clinical manifestations. However, fibrosis associated with fever unknown origin soon developed. An elevated serum level IgG4 infiltration IgG4-positive plasma cell resected pericardium were identified; thus, our patient might have hyper-IgG4 disease. Our case is first report describing constrictive pericarditis as an initial manifestation