Management of Primary Pulmonary Hypertension

摘要: Primary pulmonary hypertension represents a heterogenous group of disorders in which artery pressure and vascular resistance are markedly elevated the absence known causes {1–3}. Although disease commonly afflicts young women, patients any sex or age may be affected. Three distinct pathologic subtypes primary pumonary hyper­tension recognized by World Health Organization {4}: plexogenic arteriopathy, microthromboembolism, veno­occlusive disease, but it remains unknown whether these categories represent eti­ologies with common final clinical picture different manifestations same disease. The dilemma is made more complicated fact that can­not distinguished clinically confidence, attempts to establish diagnosis open lung biopsy risks possibility changes seen small specimen not present throughout {5}.