Pulmonary vascular disease in complete atrioventricular canal defect

摘要: The incidence and time of occurrence pulmonary vascular disease were studied in 67 children with the complete form atrioventricular (A–V) canal defect. Advanced begins to develop during first year life, intimal fibrosis (grade 3 changes) noted between age 6 months 1 year. Vascular dilatation plexiform lesions 4 can be found by These changes some patients spite hemodynamic findings usually considered indicate lesser degrees disease. After 2 years advanced is commonly may persist after surgical correction defects. A similar rapid progression was 40 who had a large ventricular septal defect without A–V whom systemic pressure transmitted directly bed. Thirty-six trisomy-21. No difference speed these those trisomy 21. Palliative or corrective surgery should performed prevent development