Exstrophy-Epispadias Complex

摘要: Bladder exstrophy is a complex congenital birth defect ranging from complete epispadias to bladder exstrophy. Though not included in the exstrophy-epispadias (EEC) disease spectrum, cloacal more severe form which includes bowel segments and has many of same defects as EEC. Initial care these patients focuses on primary repair defect, most important operations children will have their lifetime. A failure closure associated with worse outcomes across board. The essential goal treatment patient renal protection. Once that can be assured, social continence then becomes goal. Given nature this disorder, should managed at speciality centers orthopedic, urologic, nursing experience patients.