Thai (δβ)°-Thalassemia and its Lnteraction with γ-Thalassemia
作者： R. J. Trent , L. Svirklys , P. Jones
DOI: 10.3109/03630268808998017
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摘要: A variant of Southern Italian (δβ)° -thalassemia is described in a woman Thai origin. The 3′ breakpoint (δβ)°-thalas-semia located about 1 kb upstream to that (δβ)°-thalassemia and produces smaller deletion ≊ 12.5 kb. Hematological phenotype, particularly Hb F output, similar found GγAγ(δβ)°-thalassemia despite the presence coexistent γ-thalassemia effect.
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