Enhanced excretion of urinary leukotriene E4 in mevalonic aciduria is not caused by an impaired peroxisomal degradation of cysteinyl leukotrienes

作者: E. Mayatepek , B. Tiepelmann , G.F. Hoffmann

DOI: 10.1023/A:1005351215690

关键词:

摘要:

参考文章(4)
Georg F Hoffmann, Christiane Charpentier, E Mayatepek, Josette Mancini, M Leichsenring, K Michael Gibson, Priscille Divry, Martin Hrebicek, Willy Lehnert, Klaus Sartor, Friedrich K Trefz, Dietz Rating, Hans J Bremer, William L Nyhan, Clinical and biochemical phenotype in 11 patients with mevalonic aciduria. Pediatrics. ,vol. 91, pp. 915- 921 ,(1993)
L. Biardi, A. Sreedhar, A. Zokaei, N.B. Vartak, R.L. Bozeat, J.E. Shackelford, G.A. Keller, S.K. Krisans, Mevalonate kinase is predominantly localized in peroxisomes and is defective in patients with peroxisome deficiency disorders Journal of Biological Chemistry. ,vol. 269, pp. 1197- 1205 ,(1994) , 10.1016/S0021-9258(17)42242-3
E Mayatepek, W D Lehmann, J Fauler, D Tsikas, J C Frölich, R B Schutgens, R J Wanders, D Keppler, Impaired degradation of leukotrienes in patients with peroxisome deficiency disorders. Journal of Clinical Investigation. ,vol. 91, pp. 881- 888 ,(1992) , 10.1172/JCI116309
Ertan Mayatepek, Georg F. Hoffmann, Hans J. Bremer, Enhanced urinary excretion of leukotriene E4 in patients with mevalonate kinase deficiency The Journal of Pediatrics. ,vol. 123, pp. 96- 98 ,(1993) , 10.1016/S0022-3476(05)81548-3