A contradictory treatment for lysosomal storage disorders: inhibitors enhance mutant enzyme activity
作者： Jian-Qiang Fan
DOI: 10.1016/S0165-6147(03)00158-5
关键词:
摘要: … endoplasmic reticulum (ER) and degraded by ER-associated … At sub-inhibitory concentrations, potent competitive inhibitors … the secretory pathway of the ER and, ultimately, increases …
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