Young adults with paediatric liver disease: future challenges

作者: A Dhawan , M Samyn , D Joshi

DOI: 10.1136/ARCHDISCHILD-2015-309580

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摘要: Liver disease in children is rare with just over 1000 per year diagnosed the UK. However, improvements diagnosis and surgical advances, <10% of these require liver transplantation or die while waiting for an organ are not suitable transplant (LT) candidates. Post LT survivals excellent 90% 1-year survival. Hepatoblastoma biliary atresia good examples where combined medical management (including transplantation) have achieved survival compared under 20% 40 years ago. These improved to be celebrated but now created a new patient cohort childhood onset surviving adulthood. young adults had negotiate difficult phase adolescence, special human development gains could easily compromised. Liver apart from as centralised children, only three specialised centres UK Ireland, seven adult across Non-transplant hepatology care provided several regional district general hospitals. Figure 1 shows aetiology versus adults. Current training programmes do incorporate who survive into We paediatricians also responsibility further improve early detection babies large pool neonatal jaundice that we see our day-to-day practice. This article will highlight issues encounter growing up perspective hepatologist (Dr Joshi) managing In addition, recommendations Lancet commission on UK, published …

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