Connective Tissue Disease-associated Pulmonary Arterial Hypertension in the Modern Treatment Era
作者： Robin Condliffe , David G. Kiely , Andrew J. Peacock , Paul A. Corris , J. Simon R. Gibbs
DOI: 10.1164/RCCM.200806-953OC
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摘要: Rationale: Pulmonary arterial hypertension in association with connective tissue disease (CTD-PAH) has historically had a poor prognosis, 1-year survival rate among patients systemic sclerosis–associated pulmonary (SSc-PAH) of 45%. However, more therapies have become available.Objectives: To investigate the and characteristics all diagnosed CTD-PAH U.K. service.Methods: National registry incident cases consecutively between January 2001 June 2006.Measurements Main Results: Patients (429; 73% SSc-PAH) were by catheter-based approach. One- 3-year rates 78 47% for isolated SSc-PAH. Survival was worse those respiratory disease–associated SSc-PAH (3-yr survival, 28%; P = 0.005) whereas exercise-induced superior 86%; < 0.001). Age, sex, mixed venous oxygen sa...
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sci-hub.se 参考文章(21)
David B Badesch, Nicholas S Hill, Gary Burgess, Lewis J Rubin, Robyn J Barst, Nazzareno Galiè, Gerald Simonneau, SUPER Study Group, Sildenafil for pulmonary arterial hypertension associated with connective tissue disease. The Journal of Rheumatology. ,vol. 34, pp. 2417- 2422 ,(2007)
Viviane Queyrel, Eric Hachulla, David Launay, Ulrique Michon-Pasturel, Anne-Laure Fauchais, Thierry Onimus, Bernard Devulder, Fabienne Saulnier, Sophie Robin, Luc Goullard, Mohamed Hebbar, Pierre-Yves Hatron, Aerosolized iloprost in CREST syndrome related pulmonary hypertension. The Journal of Rheumatology. ,vol. 28, pp. 2252- 2256 ,(2001)
Fredrick M Wigley, Robert A Wise, Betty Chang, Barbara White, Scleroderma patients with combined pulmonary hypertension and interstitial lung disease. The Journal of Rheumatology. ,vol. 30, pp. 2398- 2405 ,(2003)
Reda E. Girgis, Stephen C. Mathai, Jerry A. Krishnan, Fredrick M. Wigley, Paul M. Hassoun, Long-term outcome of bosentan treatment in idiopathic pulmonary arterial hypertension and pulmonary arterial hypertension associated with the scleroderma spectrum of diseases Journal of Heart and Lung Transplantation. ,vol. 24, pp. 1626- 1631 ,(2005) , 10.1016/J.HEALUN.2004.12.113
Angela M. Stupi, Virginia D. Steen, Gregory R. Owens, E. Leon Barnes, Gerald P. Rodnan, Thomas A. Medsger, Pulmonary hypertension in the CREST syndrome variant of systemic sclerosis. Arthritis & Rheumatism. ,vol. 29, pp. 515- 524 ,(1986) , 10.1002/ART.1780290409
Eric Hachulla, Virginie Gressin, Loïc Guillevin, Patrick Carpentier, Elisabeth Diot, Jean Sibilia, André Kahan, Jean Cabane, Camille Francès, David Launay, Luc Mouthon, Yannick Allanore, Kiet Phong Tiev, Pierre Clerson, Pascal de Groote, Marc Humbert, Early Detection of Pulmonary Arterial Hypertension in Systemic Sclerosis A French Nationwide Prospective Multicenter Study Arthritis & Rheumatism. ,vol. 52, pp. 3792- 3800 ,(2005) , 10.1002/ART.21433
Son-Mi Chung, Chang-Keun Lee, Eun Young Lee, Bin Yoo, Sang-Do Lee, Hee-Bom Moon, Clinical aspects of pulmonary hypertension in patients with systemic lupus erythematosus and in patients with idiopathic pulmonary arterial hypertension Clinical Rheumatology. ,vol. 25, pp. 866- 872 ,(2006) , 10.1007/S10067-006-0206-5
Micah R. Fisher, Stephen C. Mathai, Hunter C. Champion, Reda E. Girgis, Traci Housten-Harris, Laura Hummers, Jerry A. Krishnan, Fredrick Wigley, Paul M. Hassoun, Clinical differences between idiopathic and scleroderma-related pulmonary hypertension Arthritis & Rheumatism. ,vol. 54, pp. 3043- 3050 ,(2006) , 10.1002/ART.22069
ET Koh, P Lee, DD Gladman, M Abu-Shakra, PULMONARY HYPERTENSION IN SYSTEMIC SCLEROSIS: AN ANALYSIS OF 17 PATIENTS Rheumatology. ,vol. 35, pp. 989- 993 ,(1996) , 10.1093/RHEUMATOLOGY/35.10.989
M H Williams, Systemic sclerosis associated pulmonary hypertension: improved survival in the current era Heart. ,vol. 92, pp. 926- 932 ,(2006) , 10.1136/HRT.2005.069484