作者: Audrey Courboulin , Benoît Ranchoux , Sylvia Cohen-Kaminsky , Frédéric Perros , Sébastien Bonnet
DOI: 10.1097/CCO.0000000000000253
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摘要: Purpose of reviewPulmonary arterial hypertension (PAH) is a rare disease with poor prognosis and no therapeutics. PAH characterized by severe remodeling precapillary pulmonary arteries, leading to increased vascular resistance, compensatory right ventricular hypertrophy,