Mitochondria in Pediatric Cardiovascular Diseases

作者: José Marín-García

DOI: 10.1007/978-1-4614-4599-9_12

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摘要: Abnormalities in cardiac mitochondrial respiratory enzymes and DNA have been found an increasing number of pediatric cases both dilated hypertrophic cardiomyopathy, giving rise to the entity known as cardiomyopathy. Also, association mitochondria defects, including mutations, with other congenital acquired diseases is increasingly recognized. Histochemical, biochemical, molecular findings cardiomyopathy; defects associated neurological disorders (“cardioneuropathies”); alterations heart are reviewed this chapter.

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