NEUROFIBROMATOSIS (VON RECKLINGHAUSEN'S DISEASE OF THE NERVOUS SYSTEM)

摘要: The PATHOLOGIC studies by von Recklinghausen covered a pleomorphic variety of disorders, but he is best known for the detailed description two disease entities which bear his name. first, frequently termed neurofibromatosis, or Recklinghausen's disease, characterized chiefly pigmentary and tumorous disorder skin, tumors nervous system fibrocystic bones. second, generalized osteitis fibrosa, bones, wholly unrelated to first disorder, with it sometimes confused. To make distinction more definite, term system, has been used former, while bone designates latter. study morbid anatomic manifestations neurofibromatosis may be unusually difficult, not only because pleomorphism lesions also