Nested Stromal-Epithelial Tumor of the Liver: A Review.

摘要: Background Nested stromal-epithelial tumor (NSET) is a rare liver tumor, which most commonly seen in the pediatric age group. To best of our knowledge, there has been no published review on this English literature so far. Summary In review, we will discuss all reported details cases, including demography, clinical presentation, molecular histogenesis, imaging, gross pathology and histopathology, immunohistochemical findings, treatment modalities, outcome NSET liver. Key message Thirty-eight cases have last 20 years literature. This produces very large calcified mass characteristically can present as Cushing syndrome. nonbiliary nonhepatocytic with biphasic differentiation into 2 components epithelial stromal cells. The cells are arranged nests mildly atypical few mitotic figures. component composed myofibroblasts desmoplastic stroma often shows ossification calcification. Immunohistochemically, positive for both mesenchymal markers. majority had benign behavior an indolent course.