Current Management of Hypoplastic Left Heart Syndrome

摘要: A diminutive, nonfunctional left ventricle with aortic atresia or severe stenosis and hypoplasia of the ascending aorta constitutes main structural abnormality in hypoplastic heart syndrome. The syndrome often presents early catastrophic hemodynamic decompensation. It is most common cause cardiac death first week life1 usually affects newborns who are otherwise normal.1,2 Hypoplastic remains a major medical surgical challenge.