AMYLO-1,6-GLUCOSIDASE ACTIVITY IN NORMAL LEUCOCYTES AND IN LEUCOCYTES OF PATIENTS WITH GLYCOGEN-STORAGE DISEASE.

作者: F. Huijing

DOI: 10.1016/0009-8981(64)90106-8

关键词:

摘要: Abstract Amylo-1,6-glucosidase or debranching enzyme is present in leucocytes of normal persons. The activity 50–100 times less than the leucocyte phosphorylase activity. In patients with glycogen-storage disease due to deficiency enzyme, no amylo-1,6-glucosidase found.

参考文章(6)
Joseph Larner, Barbara Illingworth, Gerty T. Cori, Carl F. Cori, STRUCTURE OF GLYCOGENS AND AMYLOPECTINS II. ANALYSIS BY STEPWISE ENZYMATIC DEGRADATION Journal of Biological Chemistry. ,vol. 199, pp. 641- 651 ,(1952) , 10.1016/S0021-9258(18)38502-8
W.C. Hülsmann, T.L. Oei, S. Van Creveld, PHOSPHORYLASE ACTIVITY IN LEUCOCYTES FROM PATIENTS WITH GLYCOGEN-STORAGE DISEASE The Lancet. ,vol. 278, pp. 581- 583 ,(1961) , 10.1016/S0140-6736(61)90529-3
Hibbard E. Williams, Esther M. Kendig, James B. Field, LEUKOCYTE DEBRANCHING ENZYME IN GLYCOGEN STORAGE DISEASE Journal of Clinical Investigation. ,vol. 42, pp. 656- 660 ,(1963) , 10.1172/JCI104756
J. Larner, L.H. Schliselfeld, Studies on amylo-1, 6-glucosidase. Biochimica et Biophysica Acta. ,vol. 20, pp. 53- 61 ,(1956) , 10.1016/0006-3002(56)90262-1
K. Steinitz, Hatice Bodur, Tryggve Årman, Amylo-1,6-glucosidase activity in leucocytes from patients with glycogen storage disease Clinica Chimica Acta. ,vol. 8, pp. 807- 809 ,(1963) , 10.1016/0009-8981(63)90152-9
Hibbard E. Williams, James B. Field, LOW LEUKOCYTE PHOSPHORYLASE IN HEPATIC PHOSPHORYLASE-DEFICIENT GLYCOGEN STORAGE DISEASE Journal of Clinical Investigation. ,vol. 40, pp. 1841- 1845 ,(1961) , 10.1172/JCI104408