Non-familial hemophagocytic lymphohistiocytosis.

作者: Cleto Cozzutto , Antonino Carbone , Adele Comelli , Rachele Volpe

DOI: 10.1016/S0344-0338(89)80086-X

关键词:

摘要: A case of non-familial hemophagocytic lymphohistiocytosis (HLH) is described. The patient had a chronic course being alive and doing relatively well 3 years since onset. specific pathological features this disorder are discussed with emphasis on the fact that remarkable loss lymph node structure sustained by mature lymphohistiocytic infiltrate. Erythrophagocytosis assessed as an important but not finding. Lymphocyte depletion feature lesion. presence overlapping in HLH, infection-associated syndrome (IAHS) X-linked recessive lymphoproliferative (XLS) emphasized.

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