The role of the carnitine system in myocardial fatty acid oxidation: carnitine deficiency, failing mitochondria and cardiomyopathy

作者: H. R. Scholte , I. E. M. Luyt-Houwen , M. H. M. Vaandrager-Verduin

DOI: 10.1007/978-3-662-08390-1_8

关键词:

摘要: … This subject has been reviewed by Bremer and Osmondsen (9). The rate of fatty acid oxidation in the tissues is regulated by a variety of factors such as the availability of fatty acids by …

参考文章(82)
B Steinmann, M Wang, U Exner, U Wendel, S Rampini, F Neuheiser, U Redweik, A Niederwieser, Multiple acyl-Co A dehydrogenation deficiency (MADD) in a boy with nonketotic hypoglycemia, hepatomegaly, muscle hypotonia and cardiomyopathy. Detection of N-isovalerylglutamic acid and its monoamide. Helvetica paediatrica acta. ,vol. 38, pp. 9- 26 ,(1983)
Richard L. Sabina, Judith L. Swain, Bernard M. Patten, Tetsuo Ashizawa, William E. O'Brien, Edward W. Holmes, Disruption of the Purine Nucleotide Cycle: A POTENTIAL EXPLANATION FOR MUSCLE DYSFUNCTION IN MYOADENYLATE DEAMINASE DEFICIENCY Journal of Clinical Investigation. ,vol. 66, pp. 1419- 1423 ,(1980) , 10.1172/JCI109995
P.H.E. GROOT, H.R. SCHOLTE, W.C. HÜLSMANN, Fatty acid activation: specificity, localization, and function. Advances in lipid research. ,vol. 14, pp. 75- 126 ,(1976) , 10.1016/B978-0-12-024914-5.50009-7
Yasushi Abiko, Martin M. Winbury, Antianginal Agents, Ischemic myocardium and antianginal drugs Raven Press. ,(1979)
V.W.M. Van Hinsbergh, J.H. Veerkamp, H.Th.B. Van Moerkerk, Palmitate oxidation by rat skeletal muscle mitochondria. Comparison of polarographic and radiochemical experiments. Archives of Biochemistry and Biophysics. ,vol. 190, pp. 762- 771 ,(1978) , 10.1016/0003-9861(78)90337-5
Hans R. Scholte, Inez E.M. Luyt-Houwen, Marie-Louise Dubelaar, Willem C. Huismann, The source of malonyl-CoA in rat heart. The calcium paradox releases acetyl-CoA carboxylase and not propionyl-CoA carboxylase. FEBS Letters. ,vol. 198, pp. 47- 50 ,(1986) , 10.1016/0014-5793(86)81182-6
J A Idell-Wenger, J R Neely, J T Whitmer, M J Rovetto, Control of fatty acid metabolism in ischemic and hypoxic hearts. Journal of Biological Chemistry. ,vol. 253, pp. 4305- 4309 ,(1978) , 10.1016/S0021-9258(17)34720-8
L.L. Bieber, Shawn Farrell, 18 Carnitine Acyltransferases The Enzymes. ,vol. 16, pp. 627- 644 ,(1983) , 10.1016/S1874-6047(08)60316-9