The Budd-Chiari syndrome: outcome after treatment with the transjugular intrahepatic portosystemic shunt.

摘要: Abstract Background The role of portosystemic shunting in the treatment Budd-Chiari syndrome is still under debate. Medical therapy and liver transplantation are alternative treatments. aim this study was to determine outcome a transjugular intrahepatic shunt implantation. Methods Thirty-five patients with severe Child-Pugh score 9.2±1.9, who were not responsive medical therapy, elected for treatment, which successfully accomplished 33. Eleven had fulminant/acute (history Results reduced pressure gradient from 29±7 10±4 mm Hg improved portal flow velocity 9.2±11 51±17 cm/s. Clinical symptoms as well biochemical test results significantly during 4 weeks after treatment. Three died 2 received transplants. cumulative 1- 5-year survival rate without all 93% 74%, respectively, disease 91% respectively (no deaths time period). On average, 1.4±2.2 revisions per patient needed mean follow-up 3 years 1-year probability 47%. Conclusions provides an excellent fulminant/acute, subacute, chronic syndrome. It may be regarded acute long-term management these patients.