Cogan's syndrome: achievement of complete resolution of auditory deficit with steroids

作者: P. Singh , M. Gupta , S. S. Lehl , K. Singh

DOI: 10.1136/BCR-2013-008951

关键词:

摘要: Cogan9s syndrome is a rare inflammatory disorder predominantly affecting ocular and audiovestibular apparatus. The typical picture that of non-syphilitic interstitial keratitis, while features resemble Meniere9s disease. hearing deficit often does not adequately respond to systemic steroids, which are the mainstay therapy. Cochlear implants may ameliorate this deficit, but be readily available because financial constraints in Indian subcontinent. A high index suspicion multispecialty coordination will help early initiation therapy reduce long-term morbidity. We report case entity where recovery deficits was dramatic on high-dose steroids.

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