Normal vision despite narrowing of the optic canal in fibrous dysplasia.

作者: Janice S. Lee , Edmond FitzGibbon , John A. Butman , Craig R. Dufresne , Harvey Kushner

DOI: 10.1056/NEJMOA020742

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摘要: Background Fibrous dysplasia of bone frequently involves the anterior base cranium and results in encasement optic-nerve canals. It has been assumed that such leads to constriction eventual blindness. There is controversy about whether patients should be regularly monitored or they undergo prophylactic decompression optic nerve. This question particular concern with normal vision, since risks associated surgical include Methods We studied 38 fibrous lesser wing sphenoid bone. The underwent a detailed neuro-ophthalmologic examination computed tomography face skull, reformatted measure extent involvement canal area were compared those age- sex-matched controls. Results Of patients, 15 male 23 female, their mean age was 26 years. Twelve had polyostotic fi...

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