Ebstein's Anomaly Associated with Cardiomyopathy and Pulmonary Hypertension

摘要: A patient is described with cardiomyopathy and intracavitary electrocardiographic findings typical of Ebstein's anomaly the tricuspid valve. The was characterized by extreme thickness left ventricular wall on angiocardiography, elevated end-diastolic pressures ventricles, prominent "a" waves in atrial pressure pulses. Moderately severe pulmonary hypertension, which has not previously been anomaly, also attributed to cardiomyopathy. This case illustrates increasing number associations reported emphasizes importance considering this diagnosis planning cardiac catheterization patients congenital heart disease. necessity demonstrating coexisting disease indicated formidable mortality such at surgery.