Mesenteric vein thrombosis as presenting manifestation of hereditary protein S deficiency

摘要: Protein S deficiency is inherited as an autosomal dominant trait. Heterozygotes with a reduction of 50% in the plasma protein concentration are at risk for development venous thromboembolism, often occurring early age without apparent cause. In majority patients thrombosis restricted to superficial or deep system legs. this case report we describe presence mesenteric vein 30-yr-old man hereditary deficiency. his family was also recognized mother, brother, and niece. Both mother brother had history thrombotic disease.