Does "cystic" biliary atresia represent a distinct clinical and etiological subgroup? A series of three cases.

摘要: We describe a unique series of 3 cases biliary atresia (BA) associated with choledochal cyst. All children presented jaundice at birth and had no other abnormalities. Although these fetal form BA, their presentation outcome differed from those splenic malformation syndrome (BASM), the well-described early onset BA. Unlike BASM, malformations, normal weight, did not yet require liver transplant. believe that present patients pathology may represent distinct phenotype common, prenatally acquired etiology is different forms such as who classic perinatal