Treatment of congenital pulmonary lymphangiectasia using ethiodized oil lymphangiography

摘要: Historically, congenital pulmonary lymphangiectasia (CPL) has had poor treatment outcomes despite aggressive therapy. There are recent reports of ethiodized oil (Lipiodol) lymphangiography successfully treating lymphatic leakage in adults. In this report, we describe two infants with CPL complicated by chylothoraces treated instillation into the system. Congenital atresia thoracic duct was demonstrated on lymphangiogram both patients before treatment. Both have shown good short-term without supplemental oxygen or fat restricted diets at 9 months age. Ethiodized represents a new modality for some CPL.