Hennekam syndrome: an uncommon cause of chylous ascites and intestinal lymphangiectasia in the tropics

作者: Jagadeesh Menon , Vybhav Venkatesh , Balamurugan Thirunavukkarasu , Sadhna Bhasin Lal

DOI: 10.1136/BCR-2019-229419

关键词:

摘要: Paediatric chylous ascites in tropics is commonly caused by infections and trauma. We describe the clinical characteristics of an uncommon inherited cause of chylous ascites, Hennekam syndrome, treated by nutritional modification.

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