Complex double-outlet right ventricle repair in a neonate with complete tracheal agenesis.

摘要: underline the relative greater frequency of this complication in heterotaxy syndrome when associated with anomalous pulmonary and systemic venous connections, which can make surgical repair complicated need to create a tortuous potentially obstructive pathway. Despite concern, recent report from our institution 5 has shown excellent outcome cavopulmonary connection patients return. This is likely due improved technique use extracardiac conduit cases complex atrial anatomy (18%). None 3 had evidence obstruction at pathway early after Fontan procedure, as determined by 2-dimensional echocardiography. Pulmonary developed slowly through period several months years. In patient 2, 4 device closure fenestration, suggesting that additional scarring implantation contributed obstruction. The was fibrotic tissue either interatrial septum or course veins (patient 2). To prevent complication, ensure wide open outflow, particularly mitral atresia stenosis, we currently enlarge communication between right atrium unroofing coronary sinus posteriorly into left atrium, addition resection septum. conclusion, late onset lateral tunnel rare but serious may be prevented time procedure.