The renal lesion in Wilson's disease

作者: Edward S. Reynolds , Richard L. Tannen , H.Richard Tyler

DOI: 10.1016/0002-9343(66)90116-1

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摘要: Abstract A case of hepatolenticular degeneration is reported in which the renal defect was studied physiologically and pathologically. Lesions noted chiefly proximal tubules both light electron microscopy correlated well with functional deficits. No direct relationship between copper deposits pathologic lesion could be made out.

参考文章(31)
J.Douglas Jackson, Fred G. Smith, Neil N. Litman, Charles L. Yuile, Harrison Latta, The Fanconi syndrome with cystinosis: Electron microscopy of renal biopsy specimens from five patients The American Journal of Medicine. ,vol. 33, pp. 893- 910 ,(1962) , 10.1016/0002-9343(62)90221-8
Donald Svoboda, John Higginson, ULTRASTRUCTURAL CHANGES PRODUCED BY PROTEIN AND RELATED DEFICIENCIES IN THE RAT LIVER. American Journal of Pathology. ,vol. 45, pp. 353- 379 ,(1964)
Roy W. Bonsnes, Hertha H. Taussky, ON THE COLORIMETRIC DETERMINATION OF CREATININE BY THE JAFFE REACTION Journal of Biological Chemistry. ,vol. 158, pp. 581- 591 ,(1945) , 10.1016/S0021-9258(19)51334-5
Donald A. Adams, Ralph Goldman, Morton H. Maxwell, Harrison Latta, NEPHROTIC SYNDROME ASSOCIATED WITH PENICILLAMINE THERAPY OF WILSON'S DISEASE. The American Journal of Medicine. ,vol. 36, pp. 330- 336 ,(1964) , 10.1016/0002-9343(64)90096-8
L. LAHUT UZMAN, B. HOOD, The familial nature of the amino-aciduria of Wilson's disease (hepatolenticular degeneration). The American Journal of the Medical Sciences. ,vol. 223, pp. 392- 400 ,(1952) , 10.1097/00000441-195204000-00006
Andrew Sass-Kortsak, Morris Cherniak, Douglas W. Geiger, Robert J. Slater, OBSERVATIONS ON CERULOPLASMIN IN WILSON'S DISEASE*† Journal of Clinical Investigation. ,vol. 38, pp. 1672- 1682 ,(1959) , 10.1172/JCI103945
Arnold M. Cooper, Richard D. Eckhardt, William W. Faloon, Charles S. Davidson, INVESTIGATION OF THE AMINOACIDURIA IN WILSON'S DISEASE (HEPATOLENTICULAR DEGENERATION): DEMONSTRATION OF A DEFECT IN RENAL FUNCTION. Journal of Clinical Investigation. ,vol. 29, pp. 265- 278 ,(1950) , 10.1172/JCI102254