Glucagonoma syndrome: a review and update on treatment

作者: A.M. John , R.A. Schwartz

DOI: 10.1111/JDV.13752

关键词:

摘要: Glucagonoma syndrome is defined by the presence of an alpha-cell secreting tumour pancreas, elevated levels glucagon, and a characteristic rash called necrolytic migratory erythema (NME). NME usually specific often initial finding glucagonoma syndrome, but it may occur in other settings unassociated with pancreatic (pseudoglucagonoma syndrome). must be distinguished from pseudoglucagonoma syndrome. Prompt recognition subsequent workup for can allow earlier diagnosis enhance chances favourable outcome. In particular, metastases late, so early before liver life-saving. Surgical resection definitive treatment although chemotherapeutic agents, somatostatin analogues radionuclide therapy are also employed. Herein, we offer approach to after identifying update on its current modalities.

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