CONGENITAL FACTOR X DEFICIENCY: SPECTRUM OF BLEEDING SYMPTOMS IN 32 IRANIAN PATIENTS

作者: Peyvandi , Mannucci , Lak , Abdoullahi , Zeinali

DOI: 10.1046/J.1365-2141.1998.00806.X

关键词:

摘要: The spectrum of the clinical manifestations congenital factor X deficiency was studied in 32 Iranian patients. most frequent symptom epistaxis, which occurred 72% patients, with all degrees deficiency. Other mucosal haemorrhages (e.g. haematuria, gastrointestinal bleeding) were less and mainly patients unmeasurable X. Menorrhagia half women reproductive age. Soft tissue bleeding two-thirds patients; spontaneous haematomas haemarthroses led to severe arthropathy five Bleeding from umbilical stump an unexpected finding nine This study demonstrated that tendency is correlates levels.

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