Primary fibroblasts of NDUFS4−/− mice display increased ROS levels and aberrant mitochondrial morphology
作者： Federica Valsecchi , Sander Grefte , Peggy Roestenberg , Jori Joosten-Wagenaars , Jan A.M. Smeitink
DOI: 10.1016/J.MITO.2012.12.001
关键词:
摘要: The human NDUFS4 gene encodes an accessory subunit of the first mitochondrial oxidative phosphorylation complex (CI) and, when mutated, is associated with progressive …
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