Women with inherited bleeding disorders - Challenges and strategies for improved care.

作者: Keren O. Presky , Rezan A. Kadir

DOI: 10.1016/J.THROMRES.2019.07.004

关键词:

摘要: Abstract Women with inherited bleeding disorders (IBDs) experience significant challenges in their health, personal and reproductive lives. Heavy menstrual (HMB), general symptoms, iron deficiency excessive during miscarriage, pregnancy delivery are all common complications for women IBDs. Symptoms may present childhood or adolescence, often delays to definitive diagnosis appropriate treatment due lack of recognition the prevalence impact IBDs women. This can greatly reduce quality life affected girls school work absence, social embarrassment self-consciousness being highly prevalent. The by a carrier genetic disorder also cause psychological distress partners embarking on pregnancy. Increased awareness better understanding causes approach gynaecological have improved identification who require further haemostatic testing, however many remain un-diagnosed un-treated. Education training care givers multi-disciplinary crucial enable collaborative, patient-centred including management planning advance surgery, individualised genetics counselling couples options. review discusses current strategies improve diagnosis, clinical overall life.

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