von Willebrand Disease: Diagnostic Strategies and Treatment Options.
作者： Christopher J. Ng , Jorge Di Paola
DOI: 10.1016/J.PCL.2018.02.004
关键词:
摘要: von Willebrand disease (VWD) is one of the most common inherited bleeding disorders. Since its first description in 1926, diagnosis and management VWD has significantly improved due to increasing scientific knowledge genetics biology factor (VWF). This article reviews molecular structure function VWF as well clinical symptoms, laboratory-based diagnostic workup, classification schema for VWD. It highlights current treatment options state-of-the art research
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