摘要: A case report of a 19 year old young adult male who died suddenly without any apparent clinical cause is presented. Autopsy examination revealed hypertrophied interventricular septum and left ventricle suggestive hypertrophic cardiomyopathy (HCM). About 50% cardiomyopathies are inherited as autosomal dominant disorder, sometimes associated with neuroectodermal syndromes, such neurofibromatosis pheochromocytoma. HCM one the common causes severe arrhythmias sudden death.