Clinical Manifestations and Complications
作者： Jo-David Fine , Christoph M. Lanschuetzer , Josef Stoiber , Martin Laimer , Elke Nischler
DOI: 10.1007/978-3-211-79271-1_2
关键词:
摘要: The hallmark feature of inherited EB is mechanical fragility. Invariably this associated with the development erosions. In most forms these erosions are preceded by tense blisters, which filled clear, colorless exudate. Occasionally blisters may be hemorrhagic, notably in rare Ogna subtype EBS. rather newly described subtypes characterized cleavage within uppermost portion epidermis (“suprabasal EBS subtypes”), include superficialis [3], lethal acantholytic [6], and plakophilin-1 deficiency [7], intact usually not clinically evident, making diagnosis sometimes confusing on basis skin findings alone.
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