Clinical, genetic and immunological characteristics of 40 Chinese patients with CD40 ligand deficiency
作者： Xiao Du , Wenjing Tang , Xuemei Chen , Ting Zeng , Yanping Wang
DOI: 10.1111/SJI.12798
关键词:
摘要: … in 12.5% of patients, while normal or elevated IgA levels were shown in 47.5% of patients. … Defects in the CD40/CD40L signalling result in defective isotype class switching and poor …
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