MR imaging of abdominopelvic involvement in neurofibromatosis type 1: a review of 43 patients

摘要: Background: Plexiform neurofibromas are a frequent complication of neurofibromatosis type 1. This article discusses MR imaging findings and distribution plexiform in the abdomen pelvis. Objective: To define most prevalent patterns involvement abdominopelvic Materials methods: We reviewed appearance lesions 23 male 20 female patients (median age: 16 years) with 1 neurofibromatosis. The were part multi-institutional study 300 patients. Imaging included coronal or sagittal, axial short tau inversion recovery images. Results: common was wall (n=28, 65%) lumbosacral plexus (n=27, 63%). Retroperitoneal (n=15, 35%). Lesions less often intraperitoneal (21%) (P=0.001). Pelvic disease 63%), neural canal (n=18, 42%), hydronephrosis (n=4, 9%) also noted. Target-like noted more than half Conclusion: Abdominopelvic is primarily extraperitoneal. Although plexus, retroperitoneal pelvic usually affects important organs. added information initial follow-up clinical evaluation these